Ectopia Cordis and Pentalogy of Cantrell: Report of Two Cases

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dc.contributor.authorBakacak, Murat
dc.contributor.authorBostanci, Mehmet Suhha
dc.contributor.authorSerin, Salih
dc.contributor.authorGoya, Cemil
dc.contributor.authorBakacak, Zeynep
dc.contributor.authorAvci, Fazli
dc.date.accessioned2024-04-24T17:18:03Z
dc.date.available2024-04-24T17:18:03Z
dc.date.issued2014
dc.departmentDicle Üniversitesien_US
dc.description.abstractEctopia cordis (EC) is the presence of a live, beating heart outside the thorax and is one of the most unique congenital anomalies. EC has been a weak association noted with trisomy 18 and a few cases have been associated with other chromosomal abnormalities. Pentalogy of cantrell (PC) is a rare congenital syndrome of abdominal wall defect, lower sternal defect, diaphragmatic pericardial defect, anterior diaphragmatic defect, and intracardiac abnormalities. It has a rare frequency of about 1/100,000 births. The hallmark of this syndrome is an omphalocele associated with EC. Only a few patients with the full spectrum of the pentalogy have been described. Only very few patients survive attempts at surgical repair, the main causes of death being tachyarrhythmias, bradycardia, low blood pressure, rupture of the diverticulum, and heart failure. Early diagnosis is important about discuss the option of elective termination with the parents if intracardiac anomalies of incompatible with life are noted. We report two cases of PC diagnosed in early second trimester.en_US
dc.identifier.doi10.15296/ijwhr.2014.54
dc.identifier.endpage325en_US
dc.identifier.issn2330-4456
dc.identifier.issue5en_US
dc.identifier.scopus2-s2.0-84969285697
dc.identifier.scopusqualityQ3
dc.identifier.startpage323en_US
dc.identifier.urihttps://doi.org/10.15296/ijwhr.2014.54
dc.identifier.urihttps://hdl.handle.net/11468/18570
dc.identifier.volume2en_US
dc.identifier.wosWOS:000218674100012
dc.identifier.wosqualityN/A
dc.indekslendigikaynakWeb of Science
dc.indekslendigikaynakScopus
dc.language.isoenen_US
dc.publisherAras Part Medical Int Pressen_US
dc.relation.ispartofInternational Journal of Womens Health and Reproduction Sciences
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/openAccessen_US
dc.subjectPentalogy Of Cantrellen_US
dc.subjectEctopia Cordisen_US
dc.subjectCongenital Heart Defecten_US
dc.titleEctopia Cordis and Pentalogy of Cantrell: Report of Two Casesen_US
dc.titleEctopia Cordis and Pentalogy of Cantrell: Report of Two Cases
dc.typeArticleen_US

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