External auditory canal obstruction due to tuberous sclerosis complex angiofibromas: a case report
Yükleniyor...
Tarih
2022
Yazarlar
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Springer
Erişim Hakkı
info:eu-repo/semantics/openAccess
Özet
Background: Tuberous sclerosis complex (TSC), an autosomal dominant genetic disorder and auricula and external auditory canal (EAC) involvement, is rare. Surgical excision is rarely recommended for cutaneous lesions.
Case presentation: A 31-year-old male patient was admitted with a complaint of left fullness, discharge, and conductive hearing loss. Symmetrical nodular cutaneous lesions on the malar region, tragus, and lateral portion of the EAC bilaterally were noted. The patient had diagnosed with TSC during adolescence clinically and genetically. Surgery was planned to obtain a favorable, self-cleaning EAC rather than total excision of angiofibromas. Angiofibromas on the EAC and tragus were excised. The defect was repaired by sliding a fasciocutaneous island flap inferiorly created in the preauricular area. No EAC stenosis or angiofibroma recurrence was observed during follow-up.
Discussion: Surgical excision for this clinical entity provides satisfactory management even if it was not routinely recommended for other skin lesions.
Açıklama
Anahtar Kelimeler
Tuberous sclerosis complex, Neurocutaneous syndromes, Hamartoma, External ear, Island flap
Kaynak
Egyptian Journal of Otolaryngology
WoS Q Değeri
N/A
Scopus Q Değeri
Q4
Cilt
38
Sayı
1
Künye
İşlek, A. ve Şimşek, S. (2022). External auditory canal obstruction due to tuberous sclerosis complex angiofibromas: a case report. Egyptian Journal of Otolaryngology, 38(1), 62.
