The typical appearance and CBCT images of the patient with Papillon-Lefevre syndrome: A case report

dc.contributor.authorTumen D.S.
dc.contributor.authorTumen E.C.
dc.contributor.authorGunay A.
dc.contributor.authorLacin N.
dc.contributor.authorCetin S.G.
dc.date.accessioned2024-04-24T18:46:02Z
dc.date.available2024-04-24T18:46:02Z
dc.date.issued2015
dc.departmentDicle Üniversitesien_US
dc.description.abstractPapillon-Lefevre syndrome is a rare autosomal recessive genetic disorder, which is transmitted with an estimated frequency of one to four per million individuals. It is characterized by palmar-plantar hyperkeratosis, and rapid destruction of the alveolar bone and periodontium of both the primary and permanent dentitions, commencing at the time of tooth eruption. Early diagnosed and rehabilitation of children with Papillon-Lefevre syndrome will go a long way in helping them interact normally and integrate with their peers. However, the rarity with which this entity appears, along with its complex characteristics, often make it difficult to treat. The aim of this case report is to present the early diagnosed of a 5-year-old boy with Papillon-Lefevre syndrome associated with severe periodontitis in which the premature exfoliation of primary maxillary and mandibular incisor teeth and maxillary primary first molars are observed, and with hyperkeratosis of the palms, knees and soles.en_US
dc.identifier.endpage132en_US
dc.identifier.issn1309-100X
dc.identifier.issue3en_US
dc.identifier.scopus2-s2.0-84956931002
dc.identifier.scopusqualityQ3
dc.identifier.startpage128en_US
dc.identifier.urihttps://hdl.handle.net/11468/25025
dc.identifier.volume8en_US
dc.indekslendigikaynakScopus
dc.language.isoenen_US
dc.publisherUniversity of Dicleen_US
dc.relation.ispartofJournal of International Dental and Medical Research
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.subjectPalmar-Plantar Hyperkeratosisen_US
dc.subjectPapillon-Lefevre Syndromeen_US
dc.subjectPeriodontitisen_US
dc.titleThe typical appearance and CBCT images of the patient with Papillon-Lefevre syndrome: A case reporten_US
dc.titleThe typical appearance and CBCT images of the patient with Papillon-Lefevre syndrome: A case report
dc.typeArticleen_US

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