A new patient with pyoderma gangrenosum, acne, and suppurative hidradenitis (PASH) syndrome: Case report

dc.contributor.authorAytekin S.
dc.contributor.authorUçmak D.
dc.contributor.authorAyhan E.
dc.contributor.authorFidan V.
dc.date.accessioned2024-04-24T18:45:43Z
dc.date.available2024-04-24T18:45:43Z
dc.date.issued2013
dc.departmentDicle Üniversitesien_US
dc.description.abstractPAPA syndrome is a autoinflammatory syndrome clinically characterized by pyogenic arthritis, severe acne, and pyoderma gangrenosum caused by mutations in the PSTPIP1 gene. It is a rare autosomal dominant disease of early onset. Pyoderma gangrenosum, acne and hidradenitis suppurative (PASH) syndrome has been recently identified as nonhereditary and characterized by absence of arthritis different from PAPA syndrome. No mutations have been detected to date in patients with PASH syndrome. Only three patients with PASH syndrome were reported. Herein, we report a new patient with PASH syndrome. He had severe disseminated pyoderma gangrenosum and multiple depressed scars resulting from related acne and hidradenitis suppurative but lacked any episodes of pyogenic arthritis. He was successfully treated with systemic corticosteroids. Copyright © 2013 by Türkiye Klinikleri.en_US
dc.identifier.endpage76en_US
dc.identifier.issn1300-0330
dc.identifier.issue2en_US
dc.identifier.scopus2-s2.0-84891427457
dc.identifier.scopusqualityQ4
dc.identifier.startpage73en_US
dc.identifier.urihttps://hdl.handle.net/11468/24824
dc.identifier.volume23en_US
dc.indekslendigikaynakScopus
dc.language.isoenen_US
dc.relation.ispartofTurkiye Klinikleri Dermatoloji
dc.relation.publicationcategoryKonferans Öğesi - Uluslararası - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/closedAccessen_US
dc.subjectPyoderma Gangrenosumen_US
dc.subjectPyogenic Arthritis, Pyoderma Gangrenosum And Acneen_US
dc.titleA new patient with pyoderma gangrenosum, acne, and suppurative hidradenitis (PASH) syndrome: Case reporten_US
dc.titleA new patient with pyoderma gangrenosum, acne, and suppurative hidradenitis (PASH) syndrome: Case report
dc.typeConference Objecten_US

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