Direct composite resin application, and prosthetic management in a patient with hypohidrotic ectodermal dysplasia: A case report

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Tarih

2009

Dergi Başlığı

Dergi ISSN

Cilt Başlığı

Yayıncı

Erişim Hakkı

info:eu-repo/semantics/closedAccess

Özet

Ectodermal dysplasia is a rare group of disorders affecting the nails, hair, teeth, and sweat glands to a variable degree. The most common form of ectodermal dysplasia is X-linked hypohidrotic ectodermal dysplasia, which affects males more severely, while heterozygous females exhibit variable severity, ranging from mild to severe, because of inactivation of the X-chromosome. The 7-year, 3-month-old boy presented the classical features of hypohidrotic ectodermal dysplasia, including diffusely sparse hair, eyelashes and eyebrows, severe hypohidrosis, and subsequent problems with thermoregulation, dry skin and fingernail defects. Considering the clinical situation, the age and potential growth of the young patient, a maxillary RPD and mandibular complete denture were determined to be the treatment of choice. HED is usually a difficult condition to manage prosthodontically, because of the typical oral deficiencies and afflicted individuals are quite young to receive extensive prosthodontic treatment, which restores their appearance, for the development of a positive self-image.

Açıklama

Anahtar Kelimeler

Composite Resin Restoration, Hypohidrosis, Hypohidrotic Ectodermal Dysplasia, Prosthetic Management

Kaynak

Journal of International Dental and Medical Research

WoS Q Değeri

Scopus Q Değeri

Q3

Cilt

2

Sayı

1

Künye