Xerodermapigmentosum and nursing care

Xeroderma pigmentosum (XP) is a rare hereditary disorder. It is characterized by enzymatic defects in the repair of ultraviolet-induced DNA damage, hypersensitivity of the skin to sunlight, photosensitivity, persistent erythema and hyperpigmentation. Cutaneous damage caused by ultraviolet radiation predisposes to cutaneous malignancies. This disease began at the age of 1 in our 4-year-old male patient. Our patient's clinical findings and prognosis fit the description in the literature. The nursing interventions for this case are explained.